图文详情
MFN2 agonist-1 (B-A/l) effectively induces mitochondrial fusion in cells deficient in mitofusin 2 (MFN2). It counteracts mitochondrial "clumping" (formation of static mitochondrial aggregates) and reinstates mitochondrial movement in cultured mouse neurons harboring the CMT2A-associated MFN2 T105M mutation.